Pneumothorax in a Patient with Unilateral Pulmonary Artery Agenesis
نویسندگان
چکیده
A 17-year-old Japanese woman presented with right chest pain and exertional dyspnea. The patient had a history of isolated unilateral absence of the right pulmonary artery (UAPA) and pulmonary hypertension from early childhood. Chest radiography revealed right-sided pneumothorax and a small lung volume with mediastinal and tracheal shift to the right as well as right diaphragm elevation (Picture 1). Computed tomography revealed pneumothorax and multiple thinwalled bullae only in the right lung, and absence of the right main pulmonary artery (Picture 2). The pneumothorax improved without any invasive procedures, such as needle aspiration or chest tube drainage (Picture 3). In comparison to
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